Pigmented disorders were commonly encountered in the oral cavity, varying from a focal to diffuse presentation with the varied etiological causes ranging from the exogenous to endogenous sources. Laugier-Hunziker syndrome is a rare, hereditary pigmentary disorder characterized by mucocutaneous lentiginous lesions and melanonychia. It is regarded as a diagnosis of exclusion. Here we present a case of a 70-year female with uncommon intra and extra oral pigmentation along with the melanonychia who was diagnosed with Laugier-Hunziker syndrome. Careful examination of other disorders causing the similar pigmentation has to be carefully evaluated before arriving at a final diagnosis
