The congenital malformation of the aortic arch and its branches is documented from a 45-year-old male cadaver in our case report. We recorded for the first time a right aortic arch with the following branches: left subclavian artery, common trunk of the carotid arteries, right subclavian artery. The descending aorta was located on the right side pressing the esophagus to the left. Great vessel variations are clinically important for planning surgical procedures and they could be associated with further congenital malformations, commonly with congenital heart disease. Different great vessel variations have a wide range of association with other congenital malformations, therefore, early detection with fetal echocardiography is of great importance. The described great vessel malformation was not associated with cardiac malformations nor did contribute to the death of the person. According to the accessible medical history it did not cause clinical symptoms to the patient.
